ENTRY       EC 2.4.1.88
NAME        Globoside alpha-N-acetylgalactosaminyltransferase
CLASS       Transferases
            Glycosyltransferases
            Hexosyltransferases
SYSNAME     UDP-N-acetyl-D-galactosamine:N-acetyl-D-galactosaminyl-
            $1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide
            $alpha-N-acetylgalactosaminyltransferase
REACTION    UDP-N-acetyl-D-galactosamine + N-Acetyl-D-galactosaminyl-
            $1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide = UDP +
            N-Acetyl-D-galactosaminyl-N-Acetyl-D-galactosaminyl-
            $1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide
SUBSTRATE   UDP-N-acetyl-D-galactosamine
            N-Acetyl-D-galactosaminyl-1,3-D-galactosyl-1,4-D-galactosyl-
            $1,4-D-glucosylceramide
PRODUCT     UDP
            N-Acetyl-D-galactosaminyl-N-Acetyl-D-galactosaminyl-
            $1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide
PATHWAY     PATH: MAP00600  Sphingoglycolipid metabolism
DBLINKS     University of Geneva ENZYME DATA BANK: 2.4.1.88
            WIT (What Is There) Metabolic Reconstruction: 2.4.1.88
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