ENTRY EC 2.4.1.88
NAME Globoside alpha-N-acetylgalactosaminyltransferase
CLASS Transferases
Glycosyltransferases
Hexosyltransferases
SYSNAME UDP-N-acetyl-D-galactosamine:N-acetyl-D-galactosaminyl-
$1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide
$alpha-N-acetylgalactosaminyltransferase
REACTION UDP-N-acetyl-D-galactosamine + N-Acetyl-D-galactosaminyl-
$1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide = UDP +
N-Acetyl-D-galactosaminyl-N-Acetyl-D-galactosaminyl-
$1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide
SUBSTRATE UDP-N-acetyl-D-galactosamine
N-Acetyl-D-galactosaminyl-1,3-D-galactosyl-1,4-D-galactosyl-
$1,4-D-glucosylceramide
PRODUCT UDP
N-Acetyl-D-galactosaminyl-N-Acetyl-D-galactosaminyl-
$1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide
PATHWAY PATH: MAP00600 Sphingoglycolipid metabolism
DBLINKS University of Geneva ENZYME DATA BANK: 2.4.1.88
WIT (What Is There) Metabolic Reconstruction: 2.4.1.88
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