ENTRY EC 2.4.1.62
NAME Ganglioside galactosyltransferase
UDPgalactose--ceramide galactosyltransferase
CLASS Transferases
Glycosyltransferases
Hexosyltransferases
SYSNAME UDPgalactose:N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-
$D-galactosyl-D-glucosyl-N-acylsphingosine beta-1,3-D-
$galactosyltransferase
REACTION UDPgalactose + N-Acetyl-D-galactosaminyl-(N-acetylneuraminyl)-
$D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine = UDP +
D-Galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-
$acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
SUBSTRATE UDPgalactose
N-Acetyl-D-galactosaminyl-(N-acetylneuraminyl)-
$D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
PRODUCT UDP
D-Galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-
$acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
COMMENT The substrate is also known as GM2.
PATHWAY PATH: MAP00600 Sphingoglycolipid metabolism
DBLINKS University of Geneva ENZYME DATA BANK: 2.4.1.62
WIT (What Is There) Metabolic Reconstruction: 2.4.1.62
///
DBGET integrated database retrieval system,
GenomeNet