ENTRY EC 2.4.1.18
NAME 1,4-alpha-Glucan branching enzyme
Branching enzyme
Amylo-(1,4-1,6)-transglycosylase
Q-enzyme
CLASS Transferases
Glycosyltransferases
Hexosyltransferases
SYSNAME 1,4-alpha-D-Glucan:1,4-alpha-D-glucan
6-alpha-D-(1,4-alpha-D-glucano)-transferase
REACTION Transfers a segment of a 1,4-alpha-D-glucan chain to a primary
hydroxyl group in a similar glucan chain
SUBSTRATE 1,4-alpha-D-Glucan
Amylose
Amylopectin
Glycogen
PRODUCT 6-alpha-D-(1,4-alpha-D-Glucano)-glucan
Amylopectin
COMMENT Converts amylose into amylopectin. The recommended name requires a
qualification depending on the product, glycogen or amylopectin,
e.g. glycogen branching enzyme, amylopectin branching enzyme.
The latter has frequently been termed Q-enzyme.
PATHWAY PATH: MAP00500 Starch and sucrose metabolism
DISEASE MIM: 232500 Glycogen branching enzyme; Glycogen storage disease IV
(3)
GENES ECO: b3432(glgB)
HIN: HI1357(glgB)
BSU: glgB
SYN: sll0158(glgB)
SCE: YEL011W(GLC3)
HSA: GBE1(Hs.1691)
DBLINKS University of Geneva ENZYME DATA BANK: 2.4.1.18
WIT (What Is There) Metabolic Reconstruction: 2.4.1.18
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