ENTRY       EC 2.4.1.18
NAME        1,4-alpha-Glucan branching enzyme
            Branching enzyme
            Amylo-(1,4-1,6)-transglycosylase
            Q-enzyme
CLASS       Transferases
            Glycosyltransferases
            Hexosyltransferases
SYSNAME     1,4-alpha-D-Glucan:1,4-alpha-D-glucan
            6-alpha-D-(1,4-alpha-D-glucano)-transferase
REACTION    Transfers a segment of a 1,4-alpha-D-glucan chain to a primary
            hydroxyl group in a similar glucan chain
SUBSTRATE   1,4-alpha-D-Glucan
            Amylose
            Amylopectin
            Glycogen
PRODUCT     6-alpha-D-(1,4-alpha-D-Glucano)-glucan
            Amylopectin
COMMENT     Converts amylose into amylopectin. The recommended name requires a
            qualification depending on the product, glycogen or amylopectin,
            e.g. glycogen branching enzyme, amylopectin branching enzyme.
            The latter has frequently been termed Q-enzyme.
PATHWAY     PATH: MAP00500  Starch and sucrose metabolism
DISEASE     MIM: 232500  Glycogen branching enzyme; Glycogen storage disease IV
                         (3)
GENES       ECO: b3432(glgB)
            HIN: HI1357(glgB)
            BSU: glgB
            SYN: sll0158(glgB)
            SCE: YEL011W(GLC3)
            HSA: GBE1(Hs.1691)
DBLINKS     University of Geneva ENZYME DATA BANK: 2.4.1.18
            WIT (What Is There) Metabolic Reconstruction: 2.4.1.18
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